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Riley, MS IV University of Virginia School of MedicineAAQuick Case Presentationn29 y/o female c/o chest pressure, progressive dyspnea, fatigue, swelling of face, neck, upper extremities 4 days after unsuccessful sinus mode modication, then AV node ablation and VVI pacemaker implantation for inappropriate sinus tachycardia Other PMH: Oral contraception, ex-smoker Chee CE et al. Superior vena cava syndrome: an increasingly frequent complication of cardiac procedures. Nat Clin Pract Cardiovasc Med 2007; 4: 226 230ZZZ   [      Basic Schematic of PacemakersPatient PresentationnFigure 1 Photographs of the patient showing the reduction in swelling of the face, neck and upper extremities Pn(" d2 " d2fVenograms ObtainedFigure 2 A series of venograms showing the patient's superior vena cava (A) Thrombotic occlusion was evident on presentation. (B) Thrombolysis restored patency but there was a persistent stenosis (arrow) at the superior vena cava right atrial junction, shown here at 3 month follow-up. (C), (D) Angioplasty was performed with a modest resultcC61Superior Vena Cava SyndromeFirst description by William Hunter in 1757 Sx include: edema of the upper torso including glottis edema, conjunctival suffusion (redness of the conjunctiva that is similar to conjunctivitis but without inflammatory exudates ), dyspnea*, dysphagia, headaches Cause >90% malignant <10% benign ~75% due to indwelling venous devices (PMs, ICDs, central venous catheters, etc.) Remainder are due to benign tumors, vascular anomalies causing compression, infections, etc. z ZZZZ   ,` 0SVCS as a complication of pacemaker implantation11":Incidence of pacing lead induced venous thrombosis is ~ 0.6% to 30% Incidence of symptomatic venous thrombosis is rare though, ~ 1-3% Collaterals develop if onset is slow SVCS incidence: ~ 0.2 to 3.3% of all implants Can occur at any time following implant Reported anywhere from ~ 12 hours to 15 years s/p implantZ%ZVZ:ZQ *%V:: Pathology Behind ComplicationxEndothelial disruption caused by repeated trauma from leads SVC/RA junction common site Lead bends and near intima Fibrin deposition on lead, contact to SVC wall Inflammation, fibrosis, thrombus formation, venous stenosis, occlusion No clear risk factors but potentially due to: trauma, number of leads, additional ablation, access site, lead infection, abandoned leads, etc. rXXx Radiological DiagnosisSymptoms, physical diagnosis, PMH of pacemaker/ICD implantation Invasive imaging Contrast venography is the gold-standard Non-invasive imaging Contrast-enhanced CT Doppler Ultrasonography for extremities MRI obviously contraindicated if SVCS is device relatedtQ)uQ)u$y   Treatment   Diuretics by themselves are usually inadequate Anticoagulation Mechanical thrombectomy Thrombolysis Angioplasty Stent Conservation of lead Lead extraction + re-implantation Lead extraction and no re-implantation Aftercare: Anticoagulation, anti-platelet drug therapy rx^7x^7*p   0` !3̙` Q.<ffff3` 3333fff` 3K=̙fff` 3fffff` ff3ff3` aNR>ff` 3fY33` 3f3f>?" dd@&?oAd(@n<)o<6=nA+7%Z', n?" dd@   @@``PR   = 7 ,`(p>> D<d(  d d <  #" `j   T Click to edit Master title style! !$ d 0t  "Pe   RClick to edit Master text styles Second level Third level Fourth level Fifth level!     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